Abstract
We describe a rare case of right aortic arch (RAA) and nonconfluent pulmonary arteries.
RAA and a right-sided arterial duct (AD) were identified on the prenatal scan, but
a second left-sided AD and disconnection of the left pulmonary artery were missed.
The missed diagnosis in fetal life adversely affected postnatal management. We suggest
that fetuses with a prenatal diagnosis of RAA and right-sided AD be delivered in tertiary
care centres to rule out an association with bilateral AD and nonconfluent pulmonary
arteries after birth. Prompt postnatal diagnosis will enable preservation of flow
in the disconnected pulmonary artery through prostaglandin E1 infusion until surgical
reconstruction.
Résumé
Nous décrivons un cas rare d’arc aortique droit (AAD) et d’artères pulmonaires non
confluentes. La echocardiographie prénatale a montré un AAD et un canal artériel (CA)
droit, mais n’a pas décelé le deuxième CA gauche et la déconnexion de l’artère pulmonaire
gauche. L’erreur de diagnostic au cours de la vie fœtale a des conséquences négatives
sur la prise en charge postnatale. Nous suggérons que les mères porteuses d’un fœtus
pour lequel le diagnostic prénatal montre un AAD et un CA droit soient dirigées dans
des centres de soins tertiaires pour exclure une association de CA bilatéral et d’artères
pulmonaires non confluentes après la naissance. Le diagnostic postnatal rapide permettra
de préserver le flux de l’artère pulmonaire déconnectée par la perfusion de prostaglandine
E1 jusqu’à la reconstruction chirurgicale.
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References
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Article info
Publication history
Published online: April 01, 2015
Accepted:
March 30,
2015
Received:
January 20,
2015
Footnotes
See page 1205.e2 for disclosure information.
Identification
Copyright
© 2015 Canadian Cardiovascular Society. Published by Elsevier Inc. All rights reserved.
