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Canadian Journal of Cardiology
Case Report| Volume 37, ISSUE 8, P1275-1277, August 2021

Pulmonary Embolism in a Patient With Hypertrophic Obstructive Cardiomyopathy: Think Outside “the Box”

Published:March 04, 2021DOI:https://doi.org/10.1016/j.cjca.2021.02.019

      Abstract

      A patient with hypertrophic obstructive cardiomyopathy (HOCM) was admitted with acute heart failure. Echocardiography revealed significantly worsened left ventricular outflow tract obstruction and pulmonary hypertension. Cardiac magnetic resonance imaging showed biventricular dysfunction and, as an unexpected finding, a large embolus in the right pulmonary artery. The patient gradually improved with medical therapy including oral anticoagulation. In HOCM patients, pulmonary embolism may trigger heart failure due to impaired left ventricular filling with consecutive outflow tract obstruction provocation.

      Résumé

      Un patient atteint de cardiomyopathie obstructive hypertrophique (COH) a été admis pour insuffisance cardiaque aiguë. L'échocardiographie a révélé une aggravation significative de l'obstruction de la voie d'éjection du ventricule gauche et une hypertension pulmonaire. L'imagerie par résonance magnétique cardiaque a révélé une dysfonction biventriculaire et, fait inattendu, un embole important dans l'artère pulmonaire droite. L'état du patient s'est progressivement amélioré grâce à un traitement médical comprenant une anticoagulation orale. Chez les patients atteints de COH, l'embolie pulmonaire peut déclencher une insuffisance cardiaque due à une altération du remplissage du ventricule gauche avec induction consécutive d'une obstruction de la voie d'éjection.
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