In 1992, Pedro and Josep Brugada described a typical electrocardiographic (ECG) pattern
including right bundle branch block (RBBB) and persistent ST-segment elevation associated
with sudden cardiac disease, without underlying electrolyte disturbances, ischemia,
or structural heart disease. The syndrome, which later became widely known as the
Brugada syndrome (BrS), first came to their attention in 1986 when a 3-year-old Polish
boy named Lech and his father Andreas were referred to Professor Wellens in Maastricht,
The Netherlands, owing to multiple episodes of syncope. On the ECG they observed the
typical ECG pattern that later came to be associated with the syndrome. Despite the
language barrier, they discovered that the boy had a sister who died at the age of
2 years, probably owing to cardiac arrest.
1
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Article info
Publication history
Published online: September 23, 2021
Accepted:
September 16,
2021
Received:
September 8,
2021
Footnotes
See article by Liu et al., pages 152–159 of this issue.
See page 150 for disclosure information.
Identification
Copyright
© 2021 Canadian Cardiovascular Society. Published by Elsevier Inc. All rights reserved.
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Access this article on ScienceDirectLinked Article
- A Deep Learning–Enabled Electrocardiogram Model for the Identification of a Rare Inherited Arrhythmia: Brugada SyndromeCanadian Journal of CardiologyVol. 38Issue 2
- PreviewBrugada syndrome is a major cause of sudden cardiac death in young people and has distinctive electrocardiographic (ECG) features. We aimed to develop a deep learning–enabled ECG model for automatic screening for Brugada syndrome to identify these patients at an early point in time, thus allowing for life-saving therapy.
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