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Canadian Journal of Cardiology

Primary Prevention Implantable Cardioverter-Defibrillators in Adults With Congenital Heart Disease: Recommendations From Professional Societies

  • Paul Khairy
    Correspondence
    Corresponding author: Dr Paul Khairy, Montréal Heart Institute, 5000 Belanger Street East, Montréal, Québec H1T 1C8, Canada. Tel.: +1-514-376-3330 ext 3800; fax: +1-514-593-2581.
    Affiliations
    Electrophysiology Service and Adult Congenital Heart Disease Centre, Montréal Heart Institute, Université de Montréal, Montréal, Québec, Canada
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Published:September 30, 2021DOI:https://doi.org/10.1016/j.cjca.2021.09.025
      Identifying adults with congenital heart disease (CHD) at high risk for sudden death for primary-prevention implantable cardioverter defibrillators (ICDs) remains a major challenge. Inconsistencies among professional-society recommendations are a source of confusion. This article summarizes and compares recommendations from the Canadian Cardiovascular Society (CCS) (2009), Pediatric and Congenital Electrophysiology Society (PACES) and Heart Rhythm Society (HRS) (2014), European Society of Cardiology (ESC) sudden death guidelines (2015), European Heart Rhythm Association (EHRA), Association for European Paediatric and Congenital Cardiology (AEPC), and ESC Working Group on Grown-Up CHD (2018), and ESC guidelines on adult congenital heart disease (2020). Major areas over which there is consensus are presented and scenarios with continued clinical uncertainty, which offer important opportunities for future research are highlighted.
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