|Authors||Year||n||Age||Type of palliation||Follow-up duration||Mortality||Predictors of death|
|Ammash et al.
|1996||13||Mean 42 (range 23-66) years||Eisenmenger syndrome (n = 4) and restricted pulmonary blood flow (n = 9)||Majority of patients (n = 7) seen only once; 6 patients (46%) followed 1-24 (mean 14) years||8%||Best survival: DILV with transposed great arteries and moderate degree of PS|
|Gatzoulis et al.
|2000||50||At last palliation: median 11 years (range 1 day to 53 years)||Group 1: cavopulmonary (n = 15); group 2: aortopulmonary shunt (n = 35)||Mean 13.0 ± 6.2 years after the first visit in the ACHD clinic (at age 16-18 years)||10.6% at 10 and 48.1% at 20 years after the first visit in the ACHD clinic||Predictors of death (multivariate analysis): NYHA 3 or 4 and previous episode of sustained VT; type of shunt, degree of cyanosis, and ventricular morphology were not predictive of arrhythmia or death (multivariate analysis)|
|Poterucha et al.
|2016||24||Most recent evaluation: median 52 (range 35-61) years||Pulmonary hypertension / Eisenmenger syndrome (n = 11) and restricted pulmonary blood flow (n = 13)||Median 25 (range 16-37) years||Overall mortality: 54%; Eisenmenger syndrome: 55%; restricted pulmonary blood flow: 54%||No difference between both groups (P = 0.8)|
|Erikssen et al.
|2018||111||Not available||Not specified||Not available||79%||Single dominant right ventricle (P < 0.0001)|
|Vermaut et al.
|2020||25||At Glenn: median 6.3 (IQR 1.2-29.7) years||Glenn anastomosis||Median 11 (IQR 3-18) years after Glenn procedure||20%||N/A|
|Buendía-Fuentes et al.
|2022||146||At study entry: mean 32.5 ± 11.1 years||Group 1: Eisenmenger; group 2: restricted pulmonary blood flow; group 3: aortopulmonary shunt||Mean 7.3 ± 4.1 years||Overall mortality: 22.6%; Kaplan-Meier survival analysis: 86% after 5 and 74% after 10 years||Risk factors for mortality (multivariable analysis): at least moderate AV valve regurgitation; thrombocytopenia (< 150,000/m3); renal insufficiency (eGFR < 60 mL/min/1.73 m2); QRS > 120 ms|
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See article by Buendía-Fuentes et al., pages 1111–1120 of this issue.
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