ABSTRACT
Background
Methods
Results
Conclusions
Key Words
Abbreviations:
CHD (congenital heart disease), RA (right atrium), RV (right ventricle), MELD-XI (model for end-stage liver disease excluding international normalized ratio), AUC (area under the curve), HR (hazard ratio), CI (confidence interval)Purchase one-time access:
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Conflict of Interest: none
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BRIEF SUMMARY
Of 4,977 patients, 1,376 (28%) had hepatorenal dysfunction (mild/moderate n=935[19%]; severe n=441[9%]). Hepatorenal dysfunction was most common in Fontan/unrepaired single ventricle (46%) and right heart disease (31%). Both baseline MELD-XI score and temporal changes in MELD-XI score were associated with clinical outcomes, and hence could be used to monitor for deterioration in clinical status, and therapeutic response to interventions.